Human Genetic Variation by National Institute of Health - HTML preview

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Introduction

there is considerable variation between the genomes of any two individuals,

but only a small amount of that variation appears to have any significant

biological impact, that is, produces differences in function. The Human

Genome Project, completed in 2003, illuminated the extent of human

genetic variation as well as the variations that have biological significance.

This lesson uses an examination of variation in a 1,691-base segment of

the beta globin gene to help students consider the extent of human genetic

variation at the molecular level and the relationships between genetic

variation and disease and between genetic variation and evolution.

In Advance

Web-Based Activities

Day 1, Step 12.

Day 2, Step 4.

Materials and Preparation

Photocopies and Transparencies

Equipment and Materials

• 1 copy of Master 2.1 for each student

• (Optional) Computers

• 1 copy of Master 2.2 for each student

with Internet access

• 1 copy of Master 2.3 for each student

• 1 copy of Master 2.4 for each student

• 1 copy of Master 2.5 for each student*

• 1 copy of Master 2.6 for each group

*Needed only by classes without Internet access.

Day 1, Step 12, describes an optional laboratory exercise that you may wish

to conduct to enrich your students’ understanding of molecular variation

and the methods by which it can be identified and studied. Information

about the materials you’d need is on page 77.

Follow the instructions on page 77 to get to the Web site students will use

to view the video documentary (Step 12). If you do not have Internet access,

you can use the print-based alternative (also discussed on page 77).

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DAY 1

Procedure

1. Introduce the lesson by asking students to identify the ultimate source

of the variation they investigated in Lesson 1.

Students should recognize that the ultimate source of genetic variation

is differences in DNA sequences.

2. Explain that in this lesson, students will investigate human genetic

variation at the molecular level and examine the impact of that

variation on biological function. Give one copy of Master 2.1, How

Much Variation? Beta Globin Gene—Person A, and Master 2.2, How

Much Variation? Beta Globin Gene—Person B, to each student. Explain that the sequences on these pages come from the beta globin gene in

two different people.

Hemoglobin, the oxygen carrier in blood, is composed of four

polypeptide chains, two alpha polypeptide chains and two beta

polypeptide chains. The beta globin gene encodes the amino acid

sequence for the beta chain. Person A and person B each show 1,691

nucleotides from the “sense” strand of the gene (that is, the strand

that does not serve as the template for transcription and thus has

the same base sequence as the messenger RNA, with Ts substituted

for Us). Both the sense strand of DNA and the messenger RNA are

complementary to the DNA strand that serves as the template for

transcription. We recommend that you remind students that DNA is

double-stranded, even though only one strand is shown in Masters 2.1

and 2.2. Explain that geneticists use shortcuts like this because, given

the sequence of one DNA strand, they can infer the sequence of the

complementary strand.

The beta globin gene is one of the smallest human genes that encode

a protein; the entire gene has only about 1,700 nucleotide pairs and

includes just two introns. The sequences on Masters 2.1 and 2.2 do not

show the gene’s promoter regions but begin with the first sequences

that are translated.

3. Ask students to read the paragraph at the top of each page and then

estimate the total number of bases on each page. Direct students to

write their estimate in the space provided on the masters.

The total number of bases on each page is 1,691. Students will need this

number to complete their calculations in Step 6.

73

Student Lesson 2

Human Genetic Variation

4. Remind the students that the sequences on the masters come from the

beta globin gene in two different people. Ask students what they notice

when they compare the sequence from person A with the sequence

from person B.

Students should notice that most of the sequence appears to be exactly

the same in both people. They should also notice that the bases that are

in bold are different. If necessary, point out that these bases are at the

same positions in each gene (that is, be sure that students realize that

only these two bases, located in these specific positions, are different

in the sequences from person A and person B).

5. Point out that this sequence is only 1,691 bases long and the complete

human genome is about 3 billion bases long. Ask the students how

they might use the sequences from person A and person B and the

total size of the human genome to estimate the extent of variation

(the number of bases that differ) between the two people B. Ask as

well what assumption they would be making as they arrived at

their estimate.

Students could estimate the extent of variation across the entire genome

by calculating the percentage of difference between the two sequences

shown for person A and person B, and then multiplying this percentage

by 3 billion (the approximate number of bases in the human genome).

This estimate assumes that the sequence shown displays a typical

amount of variation.

6. Give one copy of Master 2.3, How Much Variation? Doing the Math, to each student and direct the students to use the master as a guide to

estimate this value.

If your students need help completing this estimate, suggest that they

first try the example at the bottom of the master.

The proportion of sequence difference between person A and person

B is 2/1,691 = 0.001 (rounded off). To make this more concrete for

your students, note that this means that about 1 base in every 1,000 is

different. The percentage difference is 0.001 × 100 = 0.1 percent.

The total number of base differences would be 3,000,000,000 × 0.001

= 3,000,000 or, in scientific notation, 3×109×10–3 = 3×106. That is,

we could expect to find 3 million base differences in DNA sequence

between any two people.

Note that the actual number of base differences between two people is

likely somewhat higher than this because this estimate, based as it is

on the approximate size of the human genome (one copy of each of the

autosomes, plus the X, Y, and mitochondrial chromosomes), does not

take into consideration the fact that humans are diploid.

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7. Ask students what their estimates indicate about the extent of human

genetic variation at the molecular level.

Students should recognize that at the molecular level, humans are far

more alike (about 99.9 percent of the bases are the same) than they are

different (only about 0.1 percent of the bases are different). Students

should also realize, however, that even a small percentage difference

can represent a very large actual number of differences in something

as large as the human genome.

If students have difficulty reaching these conclusions, help them by

asking questions such as, “Based on this comparison, do you think that

at the molecular level, people are more alike than they are different or

vice versa?” and “How can a difference of only 0.1 percent (1 in 1,000)

result in such a large number of differences (3 million differences)?”

8. Explain that the rest of the lesson focuses on this 0.1 percent

difference between people. Ask students questions such as, “Do you

think these differences matter? What effect do you think they have?

What might affect how much a specific difference matters?”

These questions focus students’ attention on the significance of the

differences, instead of the number of differences. Remind students of

the differences among people that they observed in Lesson 1 and point

out that most of these differences have their basis in a difference in

the DNA sequence of particular genes (pierced versus nonpierced body

parts probably do not). To help them understand the magnitude of the

number of differences between their DNA and that of another person,

ask students whether they think there are 3 million differences in

appearance and biological functions between themselves and the

person sitting next to them (discussed in Step 10, below).

9. Explain that studying the beta globin gene more closely will help

students begin to answer these questions for themselves. Have

students examine the sequences on Master 2.1, Beta Globin Gene—

Person A, and Master 2.2, Beta Globin Gene—Person B, again. Explain that the regions that show bases grouped in triplets are from the

coding regions (exons) of the gene, while the other regions are from

the noncoding regions (introns). Then, ask students which of the

two base differences in bold is most likely to matter, and why.

Most eukaryotic genes are composed of both coding and noncoding

regions, which are transcribed into an initial messenger RNA. The

noncoding introns are then spliced out of the RNA; other processing

steps ultimately result in the mature messenger RNA that is translated

into protein. Students should realize that the second base difference

occurs in a noncoding region of the gene and is unlikely to have an

impact on individuals. The first difference occurs in a coding region

and is more likely to matter.

75

Student Lesson 2

Human Genetic Variation

10. Explain that although 3 million base differences sounds like a lot,

most of these differences have no significant impact on individuals,

either because they occur in a noncoding region or for another reason.

Point out that most of these 3 million differences can only be detected

A major concept

by examining the DNA sequence.

that students should

understand from Day 1

Students should now understand that while some base differences occur

of the lesson is that

in coding regions and may result in an altered amino acid sequence

in the protein coded for by a gene, others occur in noncoding regions

most genetic differences

where they likely have no impact. Point out that only a small percentage

do not affect how

of the DNA sequences in the human genome are coding sequences.

individuals function.

Furthermore, only a small percentage of the noncoding DNA sequences

are regulatory sequences such as promoters or enhancers that can

influence the amount of gene product that results from a given gene.

The remaining DNA sequences (the majority of the total DNA sequences

in the genome) have no known function. Most of the variations in DNA

sequence occur in these latter sequences and have no detectable impact.

Note: You may wish to clarify for students the reason that most

molecular variation occurs in noncoding regions. It is true that there

are more noncoding than coding regions. However, the fundamental

biological reason for the increased variability of noncoding regions is

that there is no selective pressure exerted on changes in them. Point

out that some differences that occur in noncoding regions do have an

impact. For example, several mutations within introns in the beta globin

gene cause incorrect splicing of the messenger RNA, and as a result,

several codons may be inserted into or omitted from the sequence,

leading to nonfunctional beta globin polypeptides.

If you wish to offer your students a more sophisticated understanding

of why most DNA sequence differences have no impact, extend the

discussion to include the following ideas. Even many of the differences

that occur in coding regions have no impact. Only those differences

that result in a change in amino acid sequence in a critical region of the

protein (one that affects the function of the protein) or that result in a

premature stop codon in the RNA (and thus a truncated protein) have a

significant impact on the individual carrying that variation. As students

will see in Day 2, those few differences that do affect individuals often

have devastating consequences.

11. Point out the codon in which the first difference between the

two sequences occurs and tell students that person A has normal

hemoglobin, while person B has abnormal hemoglobin that is

associated with sickle cell disease. Explain that the single base

difference in this codon determines whether a person has normal

hemoglobin or sickle hemoglobin.

If you wish, ask students to identify the actual amino acid difference

between these two types of hemoglobin, based on the difference in the

DNA sequence of the codon you identified. This is an opportunity for

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students to review the translation process and the genetic code. Remind

them that the sequence they have is the same as the messenger RNA

sequence, except it has Ts where the RNA would have Us. Normal

hemoglobin has glutamic acid (RNA codon GAG) in the position where

sickle cell hemoglobin has valine (RNA codon GUG).

12.

Step 12 for classes with access to the Internet: Tell students

that in the next part of the lesson, they will consider the

consequences of the genetic variation that results in sickle

cell disease. Hand out Master 2.4, Exploring Sickle Cell

Disease, and direct students to organize into small groups. Have

students view the documentary “What Is Sickle Cell Disease?” on

the student section of the Human Genetic Variation Web site

( http://science.education.nih.gov/supplements/genetic/student; click

on “The Meaning of Genetic Variation”) and begin working on the

questions.

Step 12 for classes using the print version: Tell students

that in the next part of the lesson, they will consider

the consequences of the genetic variation that results in

sickle cell disease. Hand out one copy each of Masters 2.4,

Exploring Sickle Cell Disease, and 2.5, Reference Database: Sickle Cell

Disease, and direct students to organize into small groups and begin

working on the questions.

Give the students about 30 minutes to complete their research. Notice

that most of the information they need is located in the Sickle Cell

Database on the Web site and, for classes using the print version, on

Master 2.5. If the students’ textbook has an adequate description of

sickle cell disease, you may wish to assign certain questions on

Master 2.4 for them to complete at home with their textbook.

13. When students reach Question 2 on Master 2.4, they should explain

how they intend to test the Lindsey twins. Give the group a copy

of the test results (Master 2.6, Results of the Lindsey Test) after the

students correctly explain the test they would have conducted.

Optional alternative to Master 2.6: Instead of giving students the

results of the test they propose in Question 2 on Master 2.4, you may

want them to complete the relevant laboratory activity themselves.

Kits are available that you can adapt to this purpose. Some use proteins

that represent hemoglobin from normal, sickle cell, and sickle cell trait

(heterozygous) individuals. The test results on Master 2.6 are based

on DNA from such individuals. If you use a kit, be sure to make this

distinction clear to students. If you plan to have your students complete

the lab, schedule an additional half to whole class period for the

activity.

77

Student Lesson 2

Human Genetic Variation

DAY 2

1. Open the second half of the lesson by directing students to meet in

their groups to complete or review their answers to the questions on

Master 2.4, Exploring Sickle Cell Disease. After they have completed

their work, convene a class discussion in which students can share

their answers to the questions.

Question 1a. What are the primary symptoms of sickle cell disease?

What happens in a person’s body to cause these symptoms?

People with sickle cell disease periodically experience symptoms that

include severe pain and fever. The symptoms occur when the sickle

hemoglobin (Hb S) inside red blood cells forms long crystals under

conditions of low oxygen concentration. The red blood cells elongate and

assume a “sickle” shape. The crystallized hemoglobin damages the cell

membranes, causing them to burst easily. The misshapen cells also clog

blood vessels. The result is the destruction of many red blood cells within

a few hours and a disruption of oxygen transport that can lead to death.

Question 1b. How is Hb S (sickle hemoglobin) different from Hb A

(normal hemoglobin)?

Sickle hemoglobin (Hb S) has the amino acid valine in the position

where normal hemoglobin (Hb A) has the amino acid glutamic acid.

Question 1c. How can this difference in hemoglobin be detected in

the laboratory?

Because of the difference in the amino acid sequence of Hb A and Hb S,

the two forms of hemoglobin have different charges. The two forms can

be separated using electrophoresis because Hb S moves more slowly in

an electric field than Hb A.

Question 1d. What does this difference in hemoglobin tell you about the

DNA of people whose cells make Hb S as compared with people whose

cells make Hb A?

The sequence of DNA that codes for hemoglobin in people whose cells

make Hb S must be different from the sequence of DNA that codes for

hemoglobin in people whose cells make Hb A. The allele that codes for

Hb A has the nucleotide A at a place where the allele that codes for Hb S

has the nucleotide T.

Question 1e. What is the difference between sickle cell disease and sickle

cell trait? Demonstrate in your answer that you understand how sickle

cell disease is inherited.

People who have sickle cell disease have inherited two alleles for sickle

cell hemoglobin, one from each of their parents. They are homozygous

for the sickle cell hemoglobin allele. People who have sickle cell trait

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index-87_1.png

have inherited one allele for sickle cell hemoglobin from one parent

and one allele for normal hemoglobin from the other parent. They are

heterozygous and usually have no symptoms.

Question 2. Use what you learned about sickle cell disease and trait to

propose a way to determine whether Ms. Lindsey’s twins have sickle cell

trait. Explain your procedure to your teacher, then use the information

provided on the handout your teacher will give you to determine the

results of the test.

Highlight the contribution

of basic science to the

Students should explain the following procedure: Collect DNA from

improvement of personal

Jason and from Sondra and treat it for analysis of alleles of the beta

and public health by

globin gene. Use gel electrophoresis to visualize the alleles present

asking your students

in each twin’s DNA. “Standards,” or controls, of DNA from people

with the normal ( Hb A) and sickle ( Hb S) alleles should be included

whether an early-20th-

for comparison. (Unless you have previously discussed restriction

century physician would

enzymes and RFLP analysis, you probably do not want to introduce

have answered Ms.

these concepts here. Instead, just explain to students that DNA isolated

Lindsey’s question in this

from individuals can be treated in ways that make different alleles show

manner. The answer, of

different gel electrophoresis patterns.)

course, is no. The fi rst

If a twin has normal hemoglobin, his or her DNA will migrate on

observation of sickle-

the gel in the same pattern as the DNA standard for the Hb A allele.

shaped cells was made in

If a twin has sickle cell disease, his or her hemoglobin will migrate

1910, but the molecular

in the pattern of the DNA standard for the Hb S allele. If a twin is

basis of the disease was

heterozygous (has sickle cell trait), his or her DNA will contain two

not worked out until

different alleles for the hemoglobin gene and show both the pattern

1949. You may also note

of the